Recurrent aggressive angiomyxoma of the vulva. A case report

Abstract

Intraduction: Aggressive angiomyxoma is a rare, benign, slow-growing, locally aggressive tumor, occurring in women in their reproductive years. Case report: A case of aggressive angiomyxoma of the vulva, clinically interpreted as a cyst, occurring in a 32-year-old female patient is presented. After incomplete removal, the tumor recurred more than ten times in the next 28 years. During the initial histopathological examination of the recurrent tumors they were misinterpreted as dermatofibroma/dermatofibrosarcoma. Differential diagnostic and therapeutical possibilities are discussed as well. Conclusion: The risk of recurrence in patients with aggressive angiomyxoma can be significantly reduced with appropriate recognition and adequate therapy.